[
  {
    "phenotype_id": "PH3390",
    "phenotype_version_id": 8410,
    "name": "Cystic Fibrosis",
    "definition": "This codelist was taken from [OpenCodelists](https://www.opencodelists.org/), created by [OpenSAFELY](https://www.opensafely.org/). We recommend viewing this Phenotype on the OpenCodelist website to view the most recent version.\n\n\nCodes indicating a diagnosis of cystic fibrosis or associated diseases such as primary ciliary dyskinesia\n\n\n© University of Oxford for the Bennett Institute for Applied Data Science 2025\\. This work may be copied freely for non\\-commercial research and study.\n\n",
    "implementation": null,
    "publications": null,
    "validation": null,
    "citation_requirements": null,
    "created": "2026-01-26T23:14:55.218838Z",
    "author": "OpenSAFELY",
    "collections": [
      {
        "name": "OpenCodelist",
        "value": 31
      },
      {
        "name": "Phenotype Library",
        "value": 18
      }
    ],
    "tags": null,
    "organisation": {
      "id": 1,
      "slug": "opensafely",
      "name": "OpenSAFELY"
    },
    "world_access": 1,
    "updated": "2026-01-26T23:14:55.214029Z",
    "references": [
      {
        "url": "https://github.com/opensafely/codelist-development/issues/30",
        "title": "GitHub issue"
      }
    ],
    "signed_off": [],
    "methodology": "This codelist is a subset of the Chronic Respiratory Disease codelist version 2020\\-04\\-10\\. \n\n\nThis codelist was created by selecting codes relating to cystic fibrosis (not screening), fibrosing colonopathy, and primary ciliary dyskinesia. Two clinicians additionally reviewed the Chronic Respiratory Disease codelist to check for any additional codes that had been missed.\n\n",
    "coding_system": [
      {
        "name": "Read codes v3",
        "value": 6
      }
    ],
    "open_codelist_id": "opensafely/cystic-fibrosis",
    "source_reference": "https://www.opencodelists.org/codelist/opensafely/cystic-fibrosis/2020-07-20",
    "concept_information": [
      {
        "concept_id": 8587,
        "concept_version_id": 16072,
        "concept_name": "opensafely/cystic-fibrosis/2020-07-20",
        "coding_system": {
          "id": 6,
          "name": "Read codes v3",
          "description": "Read codes v3"
        },
        "phenotype_id": "PH3390",
        "phenotype_version_id": 8410,
        "phenotype_name": "Cystic Fibrosis",
        "code_attribute_header": [
          "CTV3Source"
        ],
        "codes": [
          {
            "code": "C370.",
            "description": "Cystic fibrosis",
            "attributes": {
              "CTV3Source": "CTV3Map_Code_And_Term"
            }
          },
          {
            "code": "C3700",
            "description": "Cystic fibrosis with no meconium ileus",
            "attributes": {
              "CTV3Source": "CTV3Map_Code_And_Term"
            }
          },
          {
            "code": "C3701",
            "description": "Meconium ileus in cystic fibrosis",
            "attributes": {
              "CTV3Source": "CTV3Map_Code_And_Term"
            }
          },
          {
            "code": "C3702",
            "description": "Cystic fibrosis with pulmonary manifestations",
            "attributes": {
              "CTV3Source": "CTV3Map_Code_And_Term"
            }
          },
          {
            "code": "C3703",
            "description": "Cystic fibrosis with intestinal manifestations",
            "attributes": {
              "CTV3Source": "CTV3Map_Code_And_Term"
            }
          },
          {
            "code": "C370z",
            "description": "Cystic fibrosis NOS",
            "attributes": {
              "CTV3Source": "CTV3Map_Code_And_Term"
            }
          },
          {
            "code": "PK35.",
            "description": "Kartageners syndrome",
            "attributes": {
              "CTV3Source": "High_Level_SNOMED"
            }
          },
          {
            "code": "X101a",
            "description": "Primary ciliary dyskinesia - transposn ciliary microtubules",
            "attributes": {
              "CTV3Source": "High_Level_SNOMED"
            }
          },
          {
            "code": "X101b",
            "description": "Immotile cilia syndrome due to defective radial spokes",
            "attributes": {
              "CTV3Source": "High_Level_SNOMED"
            }
          },
          {
            "code": "X101c",
            "description": "Immotile cilia syndrome due to excessively long cilia",
            "attributes": {
              "CTV3Source": "High_Level_SNOMED"
            }
          },
          {
            "code": "X101d",
            "description": "Young's syndrome",
            "attributes": {
              "CTV3Source": "QOF"
            }
          },
          {
            "code": "X101e",
            "description": "Rutland ciliary disorientation syndrome",
            "attributes": {
              "CTV3Source": "High_Level_SNOMED"
            }
          },
          {
            "code": "X101X",
            "description": "Inherited mucociliary clearance defect",
            "attributes": {
              "CTV3Source": "High_Level_SNOMED"
            }
          },
          {
            "code": "X101Z",
            "description": "Primary ciliary dyskinesia",
            "attributes": {
              "CTV3Source": "High_Level_SNOMED"
            }
          },
          {
            "code": "X309R",
            "description": "Cystic fibrosis of pancreas",
            "attributes": {
              "CTV3Source": "High_Level_SNOMED"
            }
          },
          {
            "code": "XaBDb",
            "description": "Cystic fibrosis with other manifestations",
            "attributes": {
              "CTV3Source": "CTV3Map_Code_And_Term"
            }
          },
          {
            "code": "XaMzI",
            "description": "Cystic fibrosis related diabetes mellitus",
            "attributes": {
              "CTV3Source": "QOF"
            }
          },
          {
            "code": "XaQvd",
            "description": "Cystic fibrosis annual review",
            "attributes": {
              "CTV3Source": "CTV3Map_Code_And_Term"
            }
          },
          {
            "code": "XaREa",
            "description": "Liver disease due to cystic fibrosis",
            "attributes": {
              "CTV3Source": "CTV3Map_Code_And_Term"
            }
          },
          {
            "code": "XaREd",
            "description": "Fibrosing colonopathy",
            "attributes": {
              "CTV3Source": "CTV3Map_Code_And_Term"
            }
          },
          {
            "code": "XaREX",
            "description": "Arthropathy in cystic fibrosis",
            "attributes": {
              "CTV3Source": "CTV3Map_Code_And_Term"
            }
          },
          {
            "code": "XaREZ",
            "description": "Cystic fibrosis with distal intestinal obstruction syndrome",
            "attributes": {
              "CTV3Source": "CTV3Map_Code_And_Term"
            }
          },
          {
            "code": "XaXi9",
            "description": "Cystic fibrosis related cirrhosis",
            "attributes": {
              "CTV3Source": "CTV3Map_Code_And_Term"
            }
          },
          {
            "code": "XaZr7",
            "description": "Exacerbation of cystic fibrosis",
            "attributes": {
              "CTV3Source": "CTV3Map_Code_And_Term"
            }
          },
          {
            "code": "Y2710",
            "description": "Cystic fibrosis positive",
            "attributes": {
              "CTV3Source": "CTV3_Children"
            }
          }
        ]
      }
    ],
    "coding_system_release": "",
    "open_codelist_version_id": "74ccf1e1",
    "open_codelist_version_tag": "2020-07-20",
    "status": 1,
    "doi": "https://doi.org/10.48533/qcc8-eb32",
    "is_deleted": false,
    "publish_status": 2,
    "owner": "ieuan.scanlon",
    "template": {
      "id": 3,
      "name": "OpenCodelists Phenotype",
      "description": "OpenSafely's OpenCodelist Phenotype, visit https://www.opencodelists.org/ to learn more",
      "version_id": 1
    },
    "versions": [
      {
        "version_id": 8410,
        "version_name": "Cystic Fibrosis",
        "version_date": "2026-01-26T23:14:55.224787Z",
        "is_published": true,
        "is_latest": true
      }
    ]
  }
]