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Dentinogenesis Imperfecta Type 2 (MONDO:0007441)

Dentinogenesis imperfecta type 2 (DGI-2) is a rare, severe form of dentinogenesis imperfecta (DGI) and is characterized by weakness and discoloration of all teeth.

Overview

Category

musculoskeletal system disorder

mouth disorder

Ontology ID

MONDO:0007441

Internal:8831

Synonyms

Capdepont teeth

DGI-2

DI-2

dentinogenesis imperfecta type 1

dentinogenesis imperfecta, Shields type 2

dentinogenesis imperfecta, Shields type II

DGI-II

DGI1

dentinogenesis imperfecta 1

dentinogenesis imperfecta without osteogenesis imperfecta

opalescent dentin

opalescent teeth without osteogenesis imperfecta

Mapped terms

GARD:0012796

MEDGEN:424922

OMIM:125490

Orphanet:166260

UMLS:C2973527

icd11.foundation:314718507

Child terms

MONDO:0011571

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